Ebstein Anomaly

Daniel Tobler; Laura Jimenez-Juan; Andrew Crean; Rachel M Wald

doi:10.1007/978-1-4614-8875-0_15

Ebstein Anomaly

Daniel Tobler, Laura Jimenez-Juan, Andrew Crean, Rachel M Wald^*

^*Corresponding author for this work

Division of Cardiovascular Sciences (L5)

Research output: Chapter in Book/Conference proceeding › Chapter › peer-review

Abstract

Ebstein anomaly is a relatively rare lesion, which represents less than 1 % of all cases of congenital heart disease and has a prevalence of about 3–5 per 100,000 live births. Although Ebstein anomaly primarily relates to a malformation of the tricuspid valve with consequent effects on right ventricular development, there is, in fact, a wide variation of abnormalities and associated lesions which may have significant impact on disease prognosis. Ebstein anomaly is unique in that there is a broad spectrum of disease, varying from the severe neonatal form which continues to carry a dismal prognosis, even in contemporary series, to the milder form which may only become manifest in adult life, if at all.

Original language	English
Title of host publication	Cardiac CT and MRI for Adult Congenital Heart Disease
Editors	Farhood Saremi
Place of Publication	New York, NY
Publisher	Springer New York
Pages	361-372
Number of pages	12
ISBN (Electronic)	9781461488750
ISBN (Print)	9781461488743
DOIs	https://doi.org/10.1007/978-1-4614-8875-0_15
Publication status	Published - 23 Nov 2013

Keywords

cardiovascular magnetic resonance
tricuspid valve
tricuspid regurgitation
cardiac computed tomography
anterior leaflet

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

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10.1007/978-1-4614-8875-0_15

Cite this

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title = "Ebstein Anomaly",

abstract = "Ebstein anomaly is a relatively rare lesion, which represents less than 1 \% of all cases of congenital heart disease and has a prevalence of about 3–5 per 100,000 live births. Although Ebstein anomaly primarily relates to a malformation of the tricuspid valve with consequent effects on right ventricular development, there is, in fact, a wide variation of abnormalities and associated lesions which may have significant impact on disease prognosis. Ebstein anomaly is unique in that there is a broad spectrum of disease, varying from the severe neonatal form which continues to carry a dismal prognosis, even in contemporary series, to the milder form which may only become manifest in adult life, if at all.",

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T1 - Ebstein Anomaly

AU - Tobler, Daniel

AU - Jimenez-Juan, Laura

AU - Crean, Andrew

AU - Wald, Rachel M

PY - 2013/11/23

Y1 - 2013/11/23

N2 - Ebstein anomaly is a relatively rare lesion, which represents less than 1 % of all cases of congenital heart disease and has a prevalence of about 3–5 per 100,000 live births. Although Ebstein anomaly primarily relates to a malformation of the tricuspid valve with consequent effects on right ventricular development, there is, in fact, a wide variation of abnormalities and associated lesions which may have significant impact on disease prognosis. Ebstein anomaly is unique in that there is a broad spectrum of disease, varying from the severe neonatal form which continues to carry a dismal prognosis, even in contemporary series, to the milder form which may only become manifest in adult life, if at all.

AB - Ebstein anomaly is a relatively rare lesion, which represents less than 1 % of all cases of congenital heart disease and has a prevalence of about 3–5 per 100,000 live births. Although Ebstein anomaly primarily relates to a malformation of the tricuspid valve with consequent effects on right ventricular development, there is, in fact, a wide variation of abnormalities and associated lesions which may have significant impact on disease prognosis. Ebstein anomaly is unique in that there is a broad spectrum of disease, varying from the severe neonatal form which continues to carry a dismal prognosis, even in contemporary series, to the milder form which may only become manifest in adult life, if at all.

KW - cardiovascular magnetic resonance

KW - tricuspid valve

KW - tricuspid regurgitation

KW - cardiac computed tomography

KW - anterior leaflet

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DO - 10.1007/978-1-4614-8875-0_15

M3 - Chapter

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SP - 361

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BT - Cardiac CT and MRI for Adult Congenital Heart Disease

A2 - Saremi, Farhood

PB - Springer New York

CY - New York, NY

ER -

Ebstein Anomaly

Abstract

Keywords

UN SDGs

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