Outcomes of cochlear implantation in patients with neurofibromatosis type 2

Hannah J D North; Deborah Mawman; Martin O'Driscoll; Simon R Freeman; Scott A Rutherford; Andrew T King; Charlotte Hammerbeck-Ward; D Gareth Evans; Simon K W Lloyd

doi:10.1080/14670100.2016.1197587

Outcomes of cochlear implantation in patients with neurofibromatosis type 2

Hannah J D North, Deborah Mawman, Martin O'Driscoll, Simon R Freeman, Scott A Rutherford, Andrew T King, Charlotte Hammerbeck-Ward, D Gareth Evans, Simon K W Lloyd

Research output: Contribution to journal › Article › peer-review

Abstract

In neurofibromatosis type 2 (NF2) bilateral vestibular schwannomas (VS) or their treatment usually results in bilateral hearing loss. Cochlear implantation (CI) was traditionally not used in these patients due to concern that retrocochlear disease would render the implant ineffective. This paper describes the auditory outcomes of CI in 13 patients with NF2 and includes patients with untreated VS and patients undergoing VS removal with cochlear nerve preservation. The non-user rate was 7.7%. Of the active users, median CUNY score was 98%, median BKB score in quiet was 90% and median BKB score in noise was 68%. CI is a viable option in selected patients with NF2.

Original language	English
Pages (from-to)	172-177
Number of pages	6
Journal	Cochlear Implants International
Volume	17
Issue number	4
Early online date	3 Oct 2016
DOIs	https://doi.org/10.1080/14670100.2016.1197587
Publication status	Published - 2016

Keywords

Adolescent
Adult
Aged
Aged, 80 and over
Audiometry, Pure-Tone
Cochlear Implantation/methods
Cochlear Implants
Cochlear Nerve/surgery
Female
Hearing/physiology
Hearing Loss, Bilateral/etiology
Humans
Male
Middle Aged
Neurofibromatosis 2/complications
Neuroma, Acoustic/etiology
Retrospective Studies
Speech Perception/physiology
Treatment Outcome
Young Adult

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10.1080/14670100.2016.1197587

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title = "Outcomes of cochlear implantation in patients with neurofibromatosis type 2",

abstract = "In neurofibromatosis type 2 (NF2) bilateral vestibular schwannomas (VS) or their treatment usually results in bilateral hearing loss. Cochlear implantation (CI) was traditionally not used in these patients due to concern that retrocochlear disease would render the implant ineffective. This paper describes the auditory outcomes of CI in 13 patients with NF2 and includes patients with untreated VS and patients undergoing VS removal with cochlear nerve preservation. The non-user rate was 7.7%. Of the active users, median CUNY score was 98%, median BKB score in quiet was 90% and median BKB score in noise was 68%. CI is a viable option in selected patients with NF2.",

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author = "North, {Hannah J D} and Deborah Mawman and Martin O'Driscoll and Freeman, {Simon R} and Rutherford, {Scott A} and King, {Andrew T} and Charlotte Hammerbeck-Ward and Evans, {D Gareth} and Lloyd, {Simon K W}",

year = "2016",

doi = "10.1080/14670100.2016.1197587",

language = "English",

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journal = "Cochlear Implants International",

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T1 - Outcomes of cochlear implantation in patients with neurofibromatosis type 2

AU - North, Hannah J D

AU - Mawman, Deborah

AU - O'Driscoll, Martin

AU - Freeman, Simon R

AU - Rutherford, Scott A

AU - King, Andrew T

AU - Hammerbeck-Ward, Charlotte

AU - Evans, D Gareth

AU - Lloyd, Simon K W

PY - 2016

Y1 - 2016

N2 - In neurofibromatosis type 2 (NF2) bilateral vestibular schwannomas (VS) or their treatment usually results in bilateral hearing loss. Cochlear implantation (CI) was traditionally not used in these patients due to concern that retrocochlear disease would render the implant ineffective. This paper describes the auditory outcomes of CI in 13 patients with NF2 and includes patients with untreated VS and patients undergoing VS removal with cochlear nerve preservation. The non-user rate was 7.7%. Of the active users, median CUNY score was 98%, median BKB score in quiet was 90% and median BKB score in noise was 68%. CI is a viable option in selected patients with NF2.

AB - In neurofibromatosis type 2 (NF2) bilateral vestibular schwannomas (VS) or their treatment usually results in bilateral hearing loss. Cochlear implantation (CI) was traditionally not used in these patients due to concern that retrocochlear disease would render the implant ineffective. This paper describes the auditory outcomes of CI in 13 patients with NF2 and includes patients with untreated VS and patients undergoing VS removal with cochlear nerve preservation. The non-user rate was 7.7%. Of the active users, median CUNY score was 98%, median BKB score in quiet was 90% and median BKB score in noise was 68%. CI is a viable option in selected patients with NF2.

KW - Adolescent

KW - Adult

KW - Aged

KW - Aged, 80 and over

KW - Audiometry, Pure-Tone

KW - Cochlear Implantation/methods

KW - Cochlear Implants

KW - Cochlear Nerve/surgery

KW - Female

KW - Hearing/physiology

KW - Hearing Loss, Bilateral/etiology

KW - Humans

KW - Male

KW - Middle Aged

KW - Neurofibromatosis 2/complications

KW - Neuroma, Acoustic/etiology

KW - Retrospective Studies

KW - Speech Perception/physiology

KW - Treatment Outcome

KW - Young Adult

U2 - 10.1080/14670100.2016.1197587

DO - 10.1080/14670100.2016.1197587

M3 - Article

C2 - 27691934

SN - 1467-0100

VL - 17

SP - 172

EP - 177

JO - Cochlear Implants International

JF - Cochlear Implants International

IS - 4

ER -

Outcomes of cochlear implantation in patients with neurofibromatosis type 2

Abstract

Keywords

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