Progressive hemifacial atrophy with scleroderma and ipsilateral limb wasting (Parry-Romberg syndrome)

Progressive hemifacial atrophy (Parry-Romberg syndrome) is a very rare disorder characterized by a slowly progressive unilateral atrophy of the face affecting variably the skin, subcutaneous fatty tissue, muscle, connective tissue and bone (Rogers 1963). We present a 13-year-old boy in whom progressive hemifacial atrophy was accompanied by wasting of the ipsilateral arm and leg, and scleroderma.